NextGen 2024: Refractory SJIA & MAS Session Part 5
NextGen 2024: Refractory SJIA & MAS Session Part 5
International perspectives (Brazil): Presentation from Dr. Maria Teresa Terreri
NextGen 2024: Refractory SJIA & MAS Session Part 5
@SJIA_Foundation2 months ago
LVL, girl, 8 years old
SJIA diagnosis at 4 years old with typical features (fever, rash, arthritis, anemia, thrombocytosis)



Corticosteroids (including several pulse therapies) throughout the period, since 2020

MAS - IVIG, pulse therapy and cyclosporine
Currently - joint activity is maintained, using tofacitinib and leflunomide, with 17 active joints and episodes of systemic activity after infections.
Hb 11.2*; leuc 15.410 (N 65%; L 26,9%); Plaq 528,000*, ESR - 89*, CRP - 10,87*; Fibrinogen - 637*; LDH 409; Ferritine - 343
Potential alternatives:
A different anti-JAK agent? Another attempt at desensitization to tocilizumab? Association with abatacept?



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